Vascular ring due to double aortic arch as a cause of stridor and dysphagia in infancy: a case report

Diego  Davila-Flores; Christie Villasante-Villalta; Renee Montesinos-Segura; Juan Zúñiga-Meza; Henry Peralta-Santos; Luis  Vera-Talledo

doi:10.47487/apcyccv.v6i4.534

Authors

Diego Davila-Flores Instituto Nacional Cardiovascular INCOR, EsSalud, Lima, Perú. https://orcid.org/0000-0001-5084-6547
Christie Villasante-Villalta Servicio de Cardiología Pediátrica. Instituto Nacional Cardiovascular INCOR, EsSalud, Lima, Perú. https://orcid.org/0009-0005-6575-9098
Renee Montesinos-Segura Instituto Nacional Cardiovascular INCOR, EsSalud, Lima, Perú. https://orcid.org/0000-0001-5426-830X
Juan Zúñiga-Meza Servicio de Cardiología Pediátrica. Instituto Nacional Cardiovascular INCOR, EsSalud, Lima, Perú. https://orcid.org/0009-0008-9649-1743
Henry Peralta-Santos Servicio de Cirugía Cardiovascular Pediátrica. Instituto Nacional Cardiovascular-INCOR, EsSalud, Lima, Perú. https://orcid.org/0000-0002-0194-0112
Luis Vera-Talledo Servicio de Cirugía Cardiovascular Pediátrica. Instituto Nacional Cardiovascular-INCOR, EsSalud, Lima, Perú. https://orcid.org/0000-0003-3392-7235

DOI:

https://doi.org/10.47487/apcyccv.v6i4.534

Keywords:

Vascular Rings, Double Aortic Arch, Dysphagia, Stridor, Pediatrics

Abstract

A double aortic arch is a rare congenital vascular anomaly with clinical significance in the pediatric population due to its potential to cause extrinsic compression of the trachea and esophagus. It should be suspected in infants with persistent respiratory and gastrointestinal symptoms refractory to conventional treatment. We report the case of a 2-year-7-month-old boy presenting with recurrent stridor, repeated respiratory infections, and progressive dysphagia. Cardiac CT angiography revealed a complete vascular ring causing tracheoesophageal compression. Dominance of the left aortic arch was identified, and surgical section and distal ligation of the non-dominant right arch were performed, without direct intervention on the tracheoesophageal structures. At the 12-month follow-up, there was complete resolution of symptoms and nutritional recovery. This case highlights the importance of maintaining high clinical suspicion and ensuring timely referral. Even when surgical correction is delayed, appropriate intervention can reverse symptoms and improve quality of life

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