Trasplante cardiaco en paciente adulto con circulación de Fontan disfuncionante en un centro de alta complejidad cardiovascular en el Perú: reporte de caso

Roger Yoel Conde Moncada; Víctor Robles Velarde; Romel Zamudio Silva; Edwin Amado Masabel Chicoma; Sergio Martín Zavala Castillo; Franz Ronald Soplopuco Palacios

doi:10.47487/apcyccv.v7i3.607

Authors

Roger Yoel Conde Moncada Departamento de Cirugía Cardiovascular, Instituto Nacional Cardiovascular, Lima, Perú. https://orcid.org/0000-0002-2215-4524
Víctor Robles Velarde Departamento de Cirugía Cardiovascular, Instituto Nacional Cardiovascular, Lima, Perú. https://orcid.org/0000-0001-8840-3637
Romel Zamudio Silva Departamento de Cirugía Cardiovascular, Instituto Nacional Cardiovascular, Lima, Perú. https://orcid.org/0000-0001-6318-8280
Edwin Amado Masabel Chicoma Departamento de Cirugía Cardiovascular, Instituto Nacional Cardiovascular, Lima, Perú. https://orcid.org/0000-0002-9848-3543
Sergio Martín Zavala Castillo Departamento de Cirugía Cardiovascular, Instituto Nacional Cardiovascular, Lima, Perú. https://orcid.org/0000-0002-9605-4294
Franz Ronald Soplopuco Palacios Departamento de Cirugía Cardiovascular, Instituto Nacional Cardiovascular, Lima, Perú. https://orcid.org/0000-0003-2100-3537

DOI:

https://doi.org/10.47487/apcyccv.v7i3.607

Keywords:

Heart Transplantation, Fontan Procedure, Pulmonary Artery

Abstract

Fontan circulation failure represents a progressive condition associated with multiorgan dysfunction and increased morbidity and mortality. In this context, heart transplantation has become the definitive treatment for this subgroup of patients. Reported survival rates after heart transplantation in patients with Fontan circulation are approximately 80% at 1 year, 74% at 5 years, and 59% at 10 years. We present the case of a 46-year-old patient with a history of Ebstein anomaly who underwent intracardiac Fontan surgery, which progressed to progressive Fontan circulation failure, and who underwent orthotopic heart transplantation with reconstruction of the pulmonary branches.

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