Mid-ventricular hypertrophic cardiomyopathy with apical aneurysm: a multimodality imaging case report

Pavel Martinez-Dominguez; Manuel Horna-Noriega; María José Santa-Ana-Bayona; Sara Ramírez-Flores; Lucia  Horna-Regalado; Nilda Espinola-Zavaleta

doi:10.47487/apcyccv.v6i1.452

Authors

Pavel Martinez-Dominguez Departamento de Cardiología Nuclear, Instituto Nacional de Cardiología Ignacio Chávez, Ciudad de México, México; Facultad de Medicina y Ciencias Biomédicas, Universidad Autónoma de Chihuahua (UACH), Chihuahua, México. https://orcid.org/0009-0008-2821-9692
Manuel Horna-Noriega Departamento de Ecocardiografía, AUNA-Clínica Delgado, Lima, Perú. https://orcid.org/0000-0002-4601-8260
María José Santa-Ana-Bayona Departamento de Cardiología Nuclear, Instituto Nacional de Cardiología Ignacio Chávez, Ciudad de México, México. https://orcid.org/0009-0008-3476-9711
Sara Ramírez-Flores Departmento Cardiovascular Imaging. International Clinic, Lima, Perú. https://orcid.org/0000-0002-5900-0262
Lucia Horna-Regalado Universidad Peruana de Ciencias Aplicadas, Lima, Perú. https://orcid.org/0009-0004-9327-5843
Nilda Espinola-Zavaleta Departamento de Cardiología Nuclear, Instituto Nacional de Cardiología Ignacio Chávez, Ciudad de México, México; Departamento de Ecocardiografía, Centro Médico ABC, Ciudad de México, México. https://orcid.org/0000-0002-4820-1325

DOI:

https://doi.org/10.47487/apcyccv.v6i1.452

Keywords:

Echocardiography, Hypertrophy, Left Ventricular, Defibrillators, Implantable

Abstract

Mid-ventricular hypertrophic cardiomyopathy is a rare subgroup within hypertrophic cardiomyopathies that may present with apical aneurysm. This condition is associated with an increased risk of cardiac adverse events, including cardiac arrest, heart failure, thromboembolic events, or sudden cardiac death. We present a case of a 41-year-old man who presented with a history of exertional dyspnea and syncope. Multimodality imaging with echocardiography and cardiac magnetic resonance showed hypertrophy of the mid-ventricular segments with apical aneurysm. An implantable cardioverter-defibrillator was implanted to prevent sudden cardiac death.

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