Fibrosis endomiocárdica aislada de ventrículo derecho: presentación atípica de una rara enfermedad. Reporte de caso

Laura Valentina López Gutiérrez; Mauricio Andrés Murillo Moreno; Luisa Fernanda Durango; Jhon Fredy Salamanca Montilla; Clara Inés Saldarriaga Giraldo

doi:10.47487/apcyccv.v5i4.409

Authors

Laura Valentina López Gutiérrez Departamento de Cardiología, Clíni- ca CardioVID, Medellín, Colombia. https://orcid.org/0000-0001-9660-202X
Mauricio Andrés Murillo Moreno Departamento de Medicina Interna, Universidad CES, Medellín, Colombia. https://orcid.org/0000-0001-7673-4965
Luisa Fernanda Durango Clínica CardioVID, Medellín, Colombia. https://orcid.org/0000-0001-9036-8121
Jhon Fredy Salamanca Montilla Universidad Pontificia Bolivariana, Colombia. https://orcid.org/0000-0003-4628-6182
Clara Inés Saldarriaga Giraldo Departamento de Cardiología, Clínica CardioVID, Medellín, Colombia. https://orcid.org/0000-0002-5945-1127

DOI:

https://doi.org/10.47487/apcyccv.v5i4.409

Keywords:

Endomyocardial Fibrosis, Cardiomyopathy, Restrictive, Ventricular Dysfunction, Right

Abstract

Endomyocardial fibrosis or Davies disease is a rare cause of restrictive cardiomyopathy. It is characterized by the deposit of fibrous material in the endocardium that leads to quickly progressive heart failure. It most frequently affects both ventricles, with isolated involvement of the right ventricle being the least common form. The clinical presentation of this entity is based on symptoms of right heart failure, although arrhythmias and conduction disorders may also be present. The treatment is determined by the management of congestion and surgical intervention in symptomatic patients. We present the first case of endomyocardial fibrosis isolated from the right ventricle in Colombia, we describe the clinical, etiological, imaging and management characteristics in order to deliver to the medical community an approximate understanding of this disease focusing on an unusual way of presentation.

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