Dilatación severa del ventrículo izquierdo e insuficiencia mitral secundaria a ALCAPA en la infancia. Reporte de caso

Christie Villasante-Villalta; Diego  Davila-Flores; Renee  Montesinos-Segura; Zoila Rodriguez-Urtega; Judith Miranda-Rojas; José  Cornejo-Acevedo; Fernando Vargas Peláez; Fernando Chavarri-Velarde

doi:10.47487/apcyccv.v6i4.535

Authors

Christie Villasante-Villalta Instituto Nacional Cardiovascular-INCOR, EsSalud, Lima, Perú. https://orcid.org/0009-0005-6575-9098
Diego Davila-Flores Instituto Nacional Cardiovascular-INCOR, EsSalud, Lima, Perú. https://orcid.org/0000-0001-5084-6547
Renee Montesinos-Segura Instituto Nacional Cardiovascular-INCOR, EsSalud, Lima, Perú. https://orcid.org/0000-0001-5426-830X
Zoila Rodriguez-Urtega Instituto Nacional Cardiovascular-INCOR, EsSalud, Lima, Perú. https://orcid.org/0000-0002-6565-8917
Judith Miranda-Rojas Servicio de Cardiología Pediátrica, Instituto Nacional Cardiovascular-INCOR, EsSalud, Lima, Perú. https://orcid.org/0009-0006-6240-8740
José Cornejo-Acevedo Servicio de Cardiología Pediátrica, Instituto Nacional Cardiovascular-INCOR, EsSalud, Lima, Perú. https://orcid.org/0009-0006-9474-0916
Fernando Vargas Peláez Servicio de Cirugía Cardiovascular Pediátrica, Instituto Nacional Cardiovascular-INCOR, EsSalud, Lima, Perú. https://orcid.org/0009-0004-0033-979X
Fernando Chavarri-Velarde Servicio de Cirugía Cardiovascular Pediátrica, Instituto Nacional Cardiovascular-INCOR, EsSalud, Lima, Perú. https://orcid.org/0009-0005-7452-5197

DOI:

https://doi.org/10.47487/apcyccv.v6i4.535

Keywords:

Bland White Garland Syndrome, Dilated Cardiomyopathy, Mitral Valve Inssuficiency, Cardiac Surgery

Abstract

Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital heart defect, with an estimated incidence of 1 in 300,000 live births and a mortality rate approaching 90% within the first year of life if left untreated. We present the case of a three-year-old boy with progressive dyspnea, paroxysmal tachycardia, and poor weight gain, initially diagnosed with severe left ventricular dilatation and severe mitral regurgitation. Transthoracic echocardiography and cardiac computed tomography angiography confirmed the diagnosis of ALCAPA. Surgical correction included left coronary artery reimplantation and mitral valve repair. The patient was discharged without complications. At a two-year follow-up, he remained asymptomatic, with preserved left ventricular function and mild mitral regurgitation. This case highlights the importance of advanced imaging in the diagnosis and the role of surgical intervention in improving outcomes in this potentially fatal condition.

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