Ventrículo derecho de doble cámara en un paciente con miocardiopatía hipertrófica no obstructiva. Reporte de caso

Juan María Iroulart; Joaquín Ferrero; Rocío Blanco; Roshan Licht; Ana Miceli; María Natalia Pellegrini; Diego Pérez de Arenaza; Rodolfo Pizarro

doi:10.47487/apcyccv.v6i1.440

Authors

Juan María Iroulart Servicio de Cardiología, Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina. https://orcid.org/0009-0002-7264-6874
Joaquín Ferrero Servicio de Cardiología, Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina. https://orcid.org/0009-0002-2164-5732
Rocío Blanco Servicio de Cardiología, Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina. https://orcid.org/0000-0001-5806-2755
Roshan Licht Servicio de Cardiología, Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina. https://orcid.org/0009-0007-5716-2042
Ana Miceli Servicio de Cardiología, Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina. https://orcid.org/0009-0001-3294-7309
María Natalia Pellegrini Servicio de Cardiología, Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina. https://orcid.org/0009-0006-9614-4958
Diego Pérez de Arenaza Servicio de Cardiología, Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina. https://orcid.org/0000-0002-8582-5065
Rodolfo Pizarro Servicio de Cardiología, Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina. https://orcid.org/0000-0002-3393-952X

DOI:

https://doi.org/10.47487/apcyccv.v6i1.440

Keywords:

Cardiomyopathy Hypertrophic, Heart Ventricles, Diagnostic Imaging

Abstract

We present the case of a 42-year-old male patient with a history of bilateral lung transplantation and chronic graft dysfunction. The patient presented to the adult emergency department due to acute heart failure. During his stay in the emergency room and in outpatient follow-up, cardiac multi-imaging led to the diagnosis of double-chambered right ventricle with associated hypertrophic cardiomyopathy. Given the presence of advanced lung disease and poor adherence to immunosuppressant medication as well as clinical follow-ups, the patient was deemed unsuitable for re-lung transplantation. The optimization of his immunosuppressive medication was prioritized, and beta-blockers were added as part of the treatment for dynamic right ventricular outflow obstruction. He was referred to pulmonary rehabilitation, currently showing a partially favorable evolution to functional class II.

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References

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